Research
Le Syndrome De Cutis Laxa : Clinique Et Pronostic A Propos DUn Cas
Introduction: cutis laxa syndrome is a heterogeneous group of disorders rare elastic tissue; Characterized by skin laxity associated with systemic manifestations variables. Congénital or acquired. Case report: A 4-year-old chile, the last in a family of six, from a non-consanguineous marriage. No family related cases. For hospitalized pediatric pulmonary emphysema. Addressed to: ectropion of the right lower eyelid, entropion of left lower eyelid, the conjunctiva and hypertrophied hyperhémiées. anterior segment and background of normal eye. General examination evoked facies cutis laxa. precociously senile appearance; stretchable skin mobilizing easily malformation syndrome. In our patient the multiple organ damage and the lack of familial cases are in favor of an autosomal recessive form is poor prognosis. The patient died two weeks later in an array of respiratory failure. Discussion: Cutis laxa (CL), or elastolysis, is a rare, inherited or acquired connective tissue disorder in which the skin becomes inelastic and hangs loosely in folds. The clinical presentation and the mode of inheritance show considerable heterogeneity. cutis laxa is a heterogeneous group of disorders clinically and genetically. Characterized by skin laxity, skin stretch, Results from various tissue abnormalities or acquired conjonctif.
Amblyopie Fonctionnelle: Aspects Cliniques, Therapeutiques Et Pronostiques a Propos De 80 Patients” ” Fonctional Amblyopia, Clinical, Therapeutic and Prognostic Aspects : 80 Cases Report
Purpose: The aim of this study was to verify if we had a good management of amblyopia and to study its clinical, therapeutic and prognostic. Methodology: This is a retrospective study made in the service of Ophthalmology at the hospital specialties Rabat between 2000 and 2010, involving 80 patients with functional amblyopia. Results and discussion: The average age of care was 4.68 years, the majority of children had bilateral amblyopia itself 67.5%, 48.8% of average depth. All of strabismus in our series is 91.3% and Strabismus anisometropia was the dominant etiology in our series. In multivariate analysis: only the lateage and depth of amblyopia were the factors affecting the gain line of sight.
